A Study to Evaluate the Safety and Efficacy of Oral Nizubaglustat (AZ-3102) in Late-infantile and Juvenile Forms of GM1 Gangliosidosis or GM2 Gangliosidosis

Part of paid clinical trials in Oakland, California.

Sponsor
Azafaros A.G.
Study ID
NCT07082543
Phase
PHASE3
Status
Recruiting

Conditions

  • Gangliosidoses, GM2
  • Gangliosidosis, GM1

Eligibility Criteria

Sex
ALL
Age
4 Years - N/A
Healthy Volunteers
Not accepted

Interventions

  • AZ-3102 — DRUG
    Nizubaglustat
  • Placebo — DRUG
    Placebo

Study Details

An 18-month double-blind, randomized, placebo-controlled, multicenter, Phase 3 study to evaluate the safety and efficacy of oral nizubaglustat (AZ-3102) in late-infantile and juvenile forms of GM1 gangliosidosis or GM2 gangliosidosis

Key Dates

Start date
Jun 30, 2025
Status verified
Sep 2025
Primary completion
Nov 4, 2027
Completion
Nov 4, 2027

Study Design

Enrollment
75 participants (estimated)
Allocation
RANDOMIZED
Intervention model
PARALLEL
Primary purpose
TREATMENT

Arms

  • Experimental: Nizubaglustat
    Once daily oral dispersible tablets
  • Placebo Comparator: Placebo

Primary Outcome Measure

Change from baseline in total Scale for the Assessment and Rating of Ataxia (SARA) score [ Time Frame: Baseline to month 18 ]

Central Contacts

Locations (5)

FacilityCityStateZIPSite coordinators
UCSF Children's Hospital and Research Center at OaklandOaklandCalifornia94609
Veronica Cheung, CRC
510-428-3885
Caroline Hastings, MD (PRINCIPAL_INVESTIGATOR)
University of Minnesota Medical SchoolMinneapolisMinnesota55455-
Mayo Clinic Children's Center - PINRochesterMinnesota55905-
Children's Medical Center DallasDallasTexas75235-
Lysosomal Rare Disorders Research and Treatment CenterFairfaxVirginia22030-7404
Lauren Noll
571-732-4655

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