CNKSR2 Natural History Study

Part of paid clinical trials in San Francisco, California.

Sponsor
University of California, San Francisco
Study ID
NCT06500260
Status
Recruiting

Conditions

  • Developmental Dysphasia
  • Epileptic Encephalopathy, Childhood-Onset
  • X-Linked Intellectual Disability

Eligibility Criteria

Sex
ALL
Age
6 Years - 21 Years
Healthy Volunteers
Not accepted

Study Details

This prospective natural history study is being conducted to define the electroclinical, neurodevelopmental, and behavioral characteristics of CNKSR2 epilepsy aphasia syndrome (EAS) and intellectual disability (ID) in children aged 6 to 21 years old with CNKSR2 mutations. The data collected from this study will serve as an external control to eventual clinical trials examining precision medicine investigational therapeutics that aim to improve the seizure burden and neurodevelopmental outcomes in patients with CNKSR2 EAS/ID.

Key Dates

Start date
Jan 1, 2022
Status verified
Jul 2024
Primary completion
Dec 31, 2025
Completion
Dec 31, 2025

Study Design

Enrollment
15 participants (estimated)

Primary Outcome Measure

Change from baseline in functional connectivity within the epileptiform network using resting-state functional magnetic resonance imaging (fMRI). [ Time Frame: Baseline, Month 12, Month 24 ]

Central Contacts

Locations (1)

FacilityCityStateZIPSite coordinators
University of California, San Francisco (UCSF)San FranciscoCalifornia94158
Alex Fay, MD, PhD (PRINCIPAL_INVESTIGATOR)
Danilo Bernardo, MD (SUB_INVESTIGATOR)

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