Gene Therapy for Adenosine Deaminase Severe Combined Immune Deficiency Using Peripheral Blood and EFS ADA Vector

Part of paid clinical trials in Los Angeles, California.

Sponsor
University of California, Los Angeles
Study ID
NCT05432310
Phase
PHASE1/PHASE2
Status
Recruiting

Conditions

  • Adenosine Deaminase Severe Combined Immune Deficiency

Eligibility Criteria

Sex
ALL
Age
1 Month - N/A
Healthy Volunteers
Not accepted

Interventions

  • A cryopreserved formulation of autologous mPB CD34+ hematopoietic stem and progenitor cells transduced ex vivo with the EFS-ADA lentiviral vector encoding the human ADA enzyme — COMBINATION_PRODUCT
    Autologous transplantation of EFS-ADA lentiviral vector transduced, mPB CD34+ cells by central venous infusion, following reduced intensity conditioning with busulfan

Study Details

The aim of this study is to assess the safety and efficacy of autologous transplantation of hematopoietic stem cells (CD34+ cells) from mobilized peripheral blood (mPB) of ADA-deficient SCID infants and children following human ADA gene transfer by the EFS-ADA lentiviral vector. The level of gene transfer in blood cells and immune function will be measured as endpoints.

Key Dates

Start date
Jan 4, 2023
Status verified
Apr 2026
Primary completion
Nov 14, 2027
Completion
Dec 31, 2027

Study Design

Enrollment
20 participants (estimated)
Allocation
NA
Intervention model
SINGLE_GROUP
Primary purpose
TREATMENT

Arms

  • Experimental: Autologous mobilized peripheral blood (mPB) transduced with EFS ADA lentiviral vector
    Evaluate safety and efficacy of this autologous gene therapy

Primary Outcome Measure

Survival [ Time Frame: 24 months ]

Central Contacts

Locations (1)

FacilityCityStateZIPSite coordinators
University of California, Los Angeles (UCLA)Los AngelesCalifornia90095
Satiro De Oliveira, MD
310-825-6708
Augustine Fernandes, PhD
310-267-4948

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