Study of Efficacy and Safety of INC424 in Regularly Transfused Patients With Thalassemia.

Sponsor
Novartis Pharmaceuticals
Study ID
NCT02049450
Phase
PHASE2
Status
Completed

Conditions

  • Thalassemia Major

Eligibility Criteria

Sex
ALL
Age
18 Years - N/A
Healthy Volunteers
Not accepted

Interventions

  • ruxolitinib — DRUG
    Ruxolitinib was taken at a starting dose of 10 mg twice daily with dose adjustments within the range of 5 to 25 mg twice daily.

Study Details

Patients with severe thalassemia (thalassemia major) present with severe anemia that required life-long transfusion therapy, spleen enlargement that led to increased transfusion requirement, and other serious complications as early death, growth retardation, bone deformations and iron overload due to blood transfusions. Splenectomy can significantly reduce transfusion requirement in thalassemia patients, but it is associated with an increased risk of serious complications such as sepsis and thrombosis. Preliminary preclinical and clinical data suggested that JAK2 inhibition, by reducing spleen size, could improve hemoglobin levels, thereby eliminating the need for splenectomy and reducing transfusion requirement and related iron overload.

Key Dates

Start date
May 28, 2014
Status verified
Jun 2017
Primary completion
Apr 12, 2016
Completion
Apr 12, 2016

Study Design

Enrollment
30 participants (actual)
Allocation
NA
Intervention model
SINGLE_GROUP
Primary purpose
TREATMENT

Arms

  • Experimental: INC424 (ruxolitinib) - Study Treatment
    Regularly transfused adult patients with thalassemia and spleen enlargement.

Primary Outcome Measure

Change of Hematocrit Adjusted Volume of Red Blood Cells (RBC) [ Time Frame: week 6 to week 30 interval ]